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Prurit féroce, keratodermie palmo-plantaire, dystrophie ungueale, et érythrodermie avec cellules de Sezary circulantes: toxidermie ou lymphome ? |
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Pruritus, palmo-plantar keratoderma and erythroderma with Sézary cells in blood:drug induced erythroderma or lymphoma ? |
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Diagnostic:
Syndrome de Sézary
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Diagnosis:
Sézary syndrome
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Arguments
- Infiltrat lymphoïde atypique du derme superficiel
- et épidermotropisme, variables et similaires au Mycosis Fungoides
- Cellules de Sézary, varient de taille (comme dans le sang): cellules à noyaux cérebriformes
- Diag. Differentiel:
- Toxidermie
- Reticulose actinique
- Eczema
- Psoriasis
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- Aypical lymphoide infiltrate in the superficial dermis
- and epidermotropism, both vary in a similar pattern of mycosis fungoides
- Sézary cells vary in size (as they do in the blood): lymphocytes with cerebriform nucleii.
- Diff. diagnosis:
- Drug induced erythroderma
- Chronic actinic reticulosis
- Eczema
- Psoriasis
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